C18 Globotriaosylceramide-d3 (d18:1/18:0-d3)

A neuropeptide with diverse biological activities

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库存: 现货

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500ug

￥10162.00

8130.00

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货号: ajcx21918
CAS: N/A
别名: N-ω-CD3-Octadecanoyl-ceramide Trihexoside, Galα1-4Galβ1-4Glcβ-Cer(d18:1/18:0) d3, Gb3(d18:1/18:0-d3), Globotriaosylceramide-d3 (d18:1/18:0-d3)
分子式: C54H98D3NO18
分子量: 1055.4
纯度: >98%
溶解度: Chloroform:Methanol (2:1): soluble,DMSO: soluble
储存: Store at -20°C
库存: 现货

Background

C18 Globotriaosylceramide-d₃ is intended for use as an internal standard for the quantification of C18 globotriaosylceramide by GC- or LC-MS. C18 globotriaosylceramide is an endogenous sphingolipid that accumulates in the brain, heart, kidney, liver, lung, and spleen in a mouse model of Fabry disease, a lysosomal storage disorder characterized by a deficiency in the enzyme α-galactosidase A.¹ [Matreya, LLC. Catalog No. 1537]

1.Kamani, M.A., Proven?al, P., Boutin, M., et al.Glycosphingolipid storage in Fabry mice extends beyond globotriaosylceramide and is affected by ABCB1 depletionFuture Sci. OA.2(4)FS0147(2016)